• Users Online: 245
  • Print this page
  • Email this page
Year : 2019  |  Volume : 3  |  Issue : 3  |  Page : 307-310

Rare painful pediatric deformity; when surgery does harm: Case report and review of the literature

1 Department of Orthopedics, Baquba Teaching Hospital, Diyala, Baghdad, Iraq
2 Alameerat Private Hospital Kindi Street, Harthiya, Baghdad, Iraq
3 Department of Orthopedics, Ibri Regional Hospital, Al Dharia, Sultanate of Oman
4 Al-Mustansiriya University/College of Medicine, Neurosurgery Surgry, Baghdad, Iraq

Correspondence Address:
Dr. Luay M Al-Naser
Department of Orthopedics, Baquba Teaching Hospital, Diyala
Login to access the Email id

Source of Support: None, Conflict of Interest: None

DOI: 10.4103/jmsr.jmsr_20_19

Rights and Permissions

Fibrodysplasia ossificans progressiva (FOP) is a connective tissue disease that is extremely rare. Fibrous tissue in muscles, tendons, and ligaments get ossified spontaneously or damaged by a mutation of the body's repair mechanism. In this report, we present a case of FOP, which is considered one of the rarest diseases that can cause scoliosis and new bone formation around the spine and almost everywhere in the body. A 14-year-old female presented with scoliosis and limitation in spine and upper limb movements. The condition started at the age of 9 years with a painful mass in the right side of the upper back. At that time, the parents asked for medical help; a general surgeon advised and performed an excisional biopsy of the mass. Subsequently, the mass reappeared and continued to grow, covering nearly the entire back. Radiological investigations revealed a well-formed bony band extending from the right shoulder to the iliac bone posteriorly with bony formations in the left shoulder, back, medial aspects of the arms, axilla, and buttocks. FOP is an extremely challenging disorder with difficulties in both diagnosis and management, and large malformed toes with well-formed ossification anywhere in the body should raise the suspicion of the diagnosis. Any surgical intervention, including biopsy, will harm the patient and should be avoided.

Print this article     Email this article
 Next article
 Previous article
 Table of Contents

 Similar in PUBMED
   Search Pubmed for
   Search in Google Scholar for
 Related articles
 Citation Manager
 Access Statistics
 Reader Comments
 Email Alert *
 Add to My List *
 * Requires registration (Free)

 Article Access Statistics
    PDF Downloaded47    
    Comments [Add]    

Recommend this journal